Alternative Names and Classifications for LA00
This condition, identified by the ICD-11 code `LA00`, is known by several terms. It is officially classified as "Anencephaly or similar anomalies." Common clinical synonyms include anencephaly, congenital absence of the brain, and absence of the brain and skull. It is also recognized as a severe type of neural tube defect.Understanding Anencephaly or Similar Anomalies (ICD-11 Code LA00)
The ICD-11 code `LA00` represents a severe structural developmental anomaly of the nervous system. This condition arises from the failure of the neural tube to close properly during early fetal development. Infants born with this anomaly lack the formation of neural structures above the brainstem and cerebellum, including the cerebrum and cranial vault. While the skull is only partially formed, the eyes are typically normal.Factors Contributing to Anencephaly or Similar Anomalies
The primary cause of anencephaly or similar anomalies (ICD-11 code `LA00`) is the incomplete closure of the neural tube in the developing fetus. While the exact triggers are often not identified, a combination of genetic predispositions and environmental factors is suspected. Key risk factors include insufficient intake of folic acid by the mother before and during early pregnancy, exposure to certain medications during pregnancy, and specific maternal health conditions.Diagnosing Anencephaly or Similar Anomalies
Diagnosis of anencephaly or similar anomalies (ICD-11 code `LA00`) can often be made during routine prenatal care.- Prenatal Ultrasound: This imaging technique can typically detect the absence of the skull and major parts of the brain as early as the first trimester.
- Maternal Serum Screening: Blood tests performed on the mother can indicate an elevated risk for neural tube defects.
- Postnatal Examination: Following birth, the diagnosis is confirmed through a physical examination of the infant.
Accurate Coding for Anencephaly or Similar Anomalies
For accurate medical billing and record-keeping, precise ICD-11 coding is essential. The primary ICD-11 code for this condition is `LA00` (Anencephaly or similar anomalies). Specific sub-classifications are available for more detailed reporting:- `LA00.0` Anencephaly
- `LA00.1` Iniencephaly
- `LA00.2` Acephaly
- `LA00.3` Amyelencephaly
- `LA00.Y` Other specified anencephaly or similar anomalies
- `LA00.Z` Anencephaly or similar anomalies, unspecified
