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ICD Hub / Neoplasms (C00–D49) / 2A00.10 - Medulloblastoma of brain
ICD-11

ICD-11 Codes
for 2A00.10 - Medulloblastoma of brain
Teodor Jurukovski January 1, 1970
Fact checked by: Teodor Jurukovski
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Understanding the ICD-11 Code for Medulloblastoma of Brain

The official ICD-11 code for Medulloblastoma of brain is 2A00.10. This code is used for precise medical record documentation and billing. It identifies a malignant, invasive embryonal neoplasm originating in the cerebellum, predominantly affecting children and capable of spreading via cerebrospinal fluid pathways. Accurate coding ensures proper data collection for epidemiological studies and healthcare management.

Alternative Names and Clinical Synonyms for Medulloblastoma of Brain

Medulloblastoma of brain is also commonly referred to as Medulloblastoma. Other clinical synonyms and related terms include Anaplastic medulloblastoma, Classic medulloblastoma, Desmoplastic nodular medulloblastoma, Large cell medulloblastoma, and Medulloblastoma with extensive nodularity. In some contexts, it may be broadly referred to as a central primitive neuroectodermal tumour or neuroepithelioma.

Factors Contributing to Medulloblastoma of Brain

The exact cause of medulloblastoma of brain is not fully understood, but it originates from changes in the DNA of brain cells, leading to uncontrolled growth. While it can occur at any age, it is most common in young children. Certain inherited genetic syndromes are known to increase the risk of developing this condition. These include Gorlin syndrome, Li-Fraumeni syndrome, Turcot syndrome, Fanconi anemia, Rubinstein-Taybi syndrome, and conditions involving mutations in genes of the RAS signalling pathway, such as Noonan syndrome.

Clinical Overview of Medulloblastoma of Brain

Medulloblastoma of brain is a malignant, invasive embryonal neoplasm that arises from the cerebellum, the part of the brain responsible for muscle coordination, balance, and movement. It is the most common type of cancerous brain tumour in children, accounting for a significant percentage of childhood nervous system tumours. This aggressive tumour grows rapidly and has a tendency to spread through the cerebrospinal fluid pathways, though it typically does not metastasise to distant parts of the body. Histologically, it is characterised by small, round cells.

Recognising the Symptoms of Medulloblastoma of Brain

Symptoms of medulloblastoma of brain often arise due to the tumour's growth and the resulting pressure within the brain. Common signs include:
  • Headaches, often worse in the morning
  • Nausea and vomiting
  • Dizziness and unsteady walk (ataxia)
  • Poor coordination
  • Double vision
  • Lethargy or tiredness
These symptoms can develop gradually or appear more suddenly, particularly if there is obstructive hydrocephalus.

Managing Medulloblastoma of Brain

The primary treatment for medulloblastoma of brain typically begins with surgery to obtain tissue for diagnosis and to remove as much of the tumour as safely possible. Post-surgical management depends on factors such as the patient's age, the tumour's histological and molecular characteristics, and staging assessments. Treatment strategies often involve a combination of chemotherapy and craniospinal irradiation, particularly for children over a certain age. For younger children, less intensive therapies that aim to spare the brain from irradiation may be considered. Prognosis varies, with survival rates depending on risk stratification.

Frequently asked questions

What is the ICD-11 classification for Medulloblastoma of brain?
The ICD-11 code for Medulloblastoma of brain is 2A00.10. It is classified as a malignant, invasive embryonal neoplasm arising from the cerebellum.
What are the recognized histologic variants of Medulloblastoma of brain (2A00.10) in ICD-11?
The ICD-11 classification for Medulloblastoma of brain (2A00.10) includes four histologic variants: anaplastic medulloblastoma, desmoplastic/nodular medulloblastoma, large cell medulloblastoma, and medulloblastoma with extensive nodularity.
How can additional specificity be added to the ICD-11 code 2A00.10 for Medulloblastoma of brain?
Post-coordination can be used with the stem code 2A00.10 to specify laterality, specific anatomy, and histopathology.
Where is Medulloblastoma of brain (2A00.10) located within the ICD-11 classification structure?
Medulloblastoma of brain (2A00.10) is categorized under 2A00 Primary neoplasms of brain, specifically within the 2A00.1 Embryonal tumours of brain block.
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