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ICD Hub / Neoplasms (C00–D49) / 2A00.11 - Central primitive neuroectodermal tumour
ICD-11

ICD-11 Codes
for 2A00.11 - Central primitive neuroectodermal tumour
Teodor Jurukovski January 1, 1970
Fact checked by: Teodor Jurukovski
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Understanding Central Primitive Neuroectodermal Tumour

Central primitive neuroectodermal tumour (ICD-11 code 2A00.11) is a type of malignant neoplasm that originates from the neuroectoderm. The neuroectoderm is a crucial part of the early embryo that develops into the central and peripheral nervous systems. These tumours are aggressive and arise within the central nervous system.

Alternative Names for Central Primitive Neuroectodermal Tumour

This condition has been referred to by several other terms historically and in clinical practice. Common synonyms and related terms include: * Central nervous system primitive neuroectodermal tumour * CPNET * PNET (Primitive Neuroectodermal Tumour) * Brain neuroblastoma * Ependymoblastoma of brain * Ganglioneuroblastoma of brain * Medulloepithelioma * Atypical teratoid/rhabdoid tumour (historically grouped) It is important to note that the term "CNS primitive neuroectodermal tumor (CNS PNET)" is considered a historical term and is no longer the preferred classification in current medical literature.

Diagnosing Central Primitive Neuroectodermal Tumour

The diagnosis of central primitive neuroectodermal tumour involves a comprehensive evaluation. This typically includes imaging studies to identify the tumour's location and size. Definitive diagnosis often relies on histopathological examination of tissue samples obtained through biopsy or surgery. Modern diagnostic approaches increasingly incorporate molecular analysis to classify these tumours more precisely, distinguishing them from other embryonal tumours. Tumours that do not fit specific molecularly defined categories may be classified as 'not elsewhere classified' (NEC) or 'not otherwise specified' (NOS) if molecular testing is inconclusive or cannot be performed.

Managing Central Primitive Neuroectodermal Tumour

Treatment strategies for central primitive neuroectodermal tumour are typically multimodal and are determined based on the specific characteristics of the tumour, its stage, and the patient's overall health. Common treatment modalities include surgical resection to remove as much of the tumour as possible, followed by radiation therapy and chemotherapy. The specific combination and intensity of these treatments are tailored to the individual case, often in line with protocols for other high-grade central nervous system embryonal tumours.

Recognising Symptoms and Seeking Care

Patients experiencing symptoms that may indicate a central nervous system tumour should seek prompt medical attention. Symptoms can be varied and depend on the tumour's location and size, but may include persistent headaches, nausea, vomiting, vision changes, seizures, or neurological deficits such as weakness or balance problems. Early diagnosis and intervention are crucial for the best possible outcomes.

ICD-11 Code for Central Primitive Neuroectodermal Tumour

The official ICD-11 code for Central primitive neuroectodermal tumour is **2A00.11**. This code is used for accurate medical record-keeping, billing, and statistical reporting. It falls under the broader category of primary neoplasms of the brain.

Is ICD-11 Code 2A00.11 Billable?

Yes, ICD-11 code 2A00.11, representing Central primitive neuroectodermal tumour, is a billable and reportable diagnosis code. It is used by healthcare providers to report patient diagnoses for services rendered, facilitating accurate medical billing and insurance claims processing. Proper documentation supporting this diagnosis is essential for reimbursement.

Frequently asked questions

What is the ICD-11 classification meaning of Central primitive neuroectodermal tumour?
It is a malignant neoplasm originating in the neuroectoderm, which is the embryonic tissue that gives rise to the central and peripheral nervous systems and includes some glial cell precursors.
How can the ICD-11 code for Central primitive neuroectodermal tumour be further specified?
The ICD-11 code for Central primitive neuroectodermal tumour can be expanded using post-coordination to specify laterality, the specific anatomical site within the central nervous system, and associated manifestations.
Under which ICD-11 chapter and block is Central primitive neuroectodermal tumour classified?
Central primitive neuroectodermal tumour is classified under Chapter 02 Neoplasms, within the block for Neoplasms of brain or central nervous system (2A00-2A0Z).
What is the assumed behavior for neoplasms classified under 2A00-2A0Z in ICD-11?
For neoplasms classified within the 2A00-2A0Z range, including Central primitive neuroectodermal tumour, the behavior is presumed to be malignant unless otherwise specified.
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