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ICD Hub / Neoplasms (C00–D49) / 2A00.4 - Astroblastoma of the brain
ICD-11

ICD-11 Codes
for 2A00.4 - Astroblastoma of the brain
Teodor Jurukovski January 1, 1970
Fact checked by: Teodor Jurukovski
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Understanding Astroblastoma of the Brain (ICD-11 Code 2A00.4)

Astroblastoma of the brain, identified by the ICD-11 code 2A00.4, is a rare type of glial neoplasm that originates within the central nervous system. This condition typically presents as a well-circumscribed astrocytic tumour, most commonly found in the supratentorial region of the brain, often peripherally located within the frontal or parietal lobes. While it can occur at any age, it predominantly affects infants, children, and young adults. The cells exhibit characteristics suggestive of astrocytic origin and are often arranged in a perivascular pattern.

How Astroblastoma of the Brain is Diagnosed

The diagnosis of astroblastoma of the brain (ICD-11 code 2A00.4) relies on a combination of clinical evaluation and diagnostic imaging. Magnetic Resonance Imaging (MRI) and Computed Tomography (CT) scans are crucial for visualising the tumour's location, size, and characteristics within the brain. Definitive diagnosis is typically established through a biopsy, followed by histopathological examination. This examination identifies characteristic tumour cells, often positive for Glial Fibrillary Acidic Protein (GFAP), and their specific perivascular arrangement. Accurate coding for billing and documentation requires precise identification of this ICD-11 code.

Common Symptoms and Presentation of Astroblastoma

The clinical presentation of astroblastoma of the brain (ICD-11 code 2A00.4) varies depending on the tumour's size and precise location within the brain. Common symptoms reported by patients include persistent headaches and epileptic seizures. Other potential signs and symptoms may encompass vomiting and episodes of loss of consciousness. Neurological deficits can also occur, reflecting the tumour's impact on specific brain functions. Understanding these patient-friendly terms is vital for accurate reporting.

Causes and Risk Factors for Astroblastoma

The exact causes and specific risk factors for developing astroblastoma of the brain (ICD-11 code 2A00.4) are not fully understood due to its rarity. It is classified as a glial neoplasm, suggesting its origin from glial cells within the central nervous system. Research into the specific cellular origins and genetic alterations, such as the MN1::BEND2 fusion, is ongoing to better elucidate the aetiology of this rare brain tumour. Currently, there are no widely established environmental or lifestyle risk factors.

Treatment and Management Considerations for Astroblastoma

Management strategies for astroblastoma of the brain (ICD-11 code 2A00.4) are guided by the tumour's characteristics, including its grade and whether it is a recurrent case. Treatment typically involves a multidisciplinary approach. Surgical resection aims to remove as much of the tumour as safely possible. Adjuvant therapies, such as radiation therapy and chemotherapy, are often recommended for high-grade or recurrent tumours, although their effectiveness can be variable and is a subject of ongoing study. Careful documentation of treatment plans is essential for accurate medical records and billing.

Documentation and Coding for Astroblastoma of the Brain

Accurate medical documentation and coding are critical for reporting and billing purposes related to astroblastoma of the brain. The definitive ICD-11 code for this condition is 2A00.4. Healthcare providers should ensure that all diagnostic findings, clinical assessments, and treatment procedures are thoroughly documented to support the use of this specific ICD-11 code. This ensures precise record-keeping for this rare brain tumour and facilitates appropriate billing and statistical analysis.

Frequently asked questions

What is the ICD-11 classification for Astroblastoma of the brain (2A00.4)?
Astroblastoma of the brain (2A00.4) is classified as a rare glial neoplasm characterized by tumor cells with features suggestive of astrocytic origin, arranged perivascularly with broad, non-tapering processes radiating towards a central blood vessel.
What are the defining histological characteristics of Astroblastoma of the brain (2A00.4) in ICD-11?
In ICD-11, Astroblastoma of the brain (2A00.4) is defined by tumor cells exhibiting astrocytic origin characteristics and a perivascular arrangement, with broad, non-tapering processes radiating towards a central blood vessel.
How can the ICD-11 code 2A00.4 for Astroblastoma of the brain be further specified?
The ICD-11 code 2A00.4 for Astroblastoma of the brain can be specified using post-coordination with codes for laterality (e.g., left, right, unspecified) and specific anatomical sites within the brain. Manifestations, such as chronic cancer pain, can also be added.
What does the ICD-11 classification mean by "astroblastoma of unspecified site"?
"Astroblastoma of unspecified site" is a synonym used in ICD-11 for Astroblastoma of the brain (2A00.4) when the specific anatomical location within the brain is not documented or coded.
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