ICD-11 Codes
for LA00.3 - Amyelencephaly

Teodor Jurukovski January 1, 1970

Fact checked by: Teodor Jurukovski

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Understanding Amyelencephaly (ICD-11 Code LA00.3)

Amyelencephaly is a severe congenital anomaly affecting the nervous system. The official ICD-11 code for this condition is LA00.3. This diagnosis falls under the broader category of neural tube defects, representing a significant developmental malformation.

What is Amyelencephaly?

Amyelencephaly is specifically defined as the complete absence of both the brain and the spinal cord. It is a critical malformation of the central nervous system that occurs during embryonic development due to the failure of the neural tube to close properly.

Potential Factors Associated with Neural Tube Defects

While specific causes for amyelencephaly are not always identified, it is understood as a type of neural tube defect. Such conditions are often multifactorial, potentially resulting from a complex interplay of genetic and environmental factors. Known risk factors for neural tube defects in general include deficiencies in essential nutrients like folic acid and zinc, as well as maternal health conditions such as obesity.

Diagnosing Severe Congenital Anomalies

The diagnosis of severe congenital anomalies like amyelencephaly typically involves comprehensive medical evaluation. Prenatal screening and diagnostic imaging techniques are crucial for identifying such conditions during pregnancy. Postnatal assessment confirms the extent of the malformation.

Accurate ICD-11 Coding for Amyelencephaly (LA00.3)

For accurate medical billing and documentation, the specific ICD-11 code LA00.3 must be used for Amyelencephaly. This code is part of the 'Anencephaly or similar anomalies' block within the International Classification of Diseases, 11th Revision. Proper coding ensures precise reporting of this condition.

Amyelencephaly within the Spectrum of Anencephaly Anomalies

Amyelencephaly (LA00.3) is classified alongside other severe nervous system malformations under the ICD-11 code LA00, 'Anencephaly or similar anomalies'. This category includes conditions such as Anencephaly (LA00.0), Iniencephaly (LA00.1), and Acephaly (LA00.2), all representing significant failures in early neural development.